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我院自1954～1982年间共收治本病71例,其中Marie共济失调(MA)50例、遗传性痉挛性截瘫(HSP)9例、进行性小脑变性(PCD)和Friedreich共济失调(FA)各6例,现报道如下。临床资料一、一般资料:本组男50例,女21例。MA发病年龄为12～52岁,HSP 6～27岁,FA15～27岁,PCD42～56岁。本组病期在4年以内者42例,5～10年老24例,11年以上者5例。本组24例有遗传史,其中父系遗传者8例、母系遗传者11例,2例的弟妹和1例的姑妈是同
71 cases were treated in our hospital from 1954 to 1982, including 50 cases of atherosclerosis (MA), 9 cases of hereditary spastic paraplegia (HSP), progressive cerebellar degeneration (PCD) and Friedreich’s ataxia (FA ) Each 6 cases, are reported below. Clinical data First, the general information: The group of 50 men and 21 women. MA age of 12 to 52 years old, HSP 6 to 27 years old, FA15 to 27 years old, PCD42 to 56 years old. This group of 42 patients with disease within 4 years, 5 to 10 years old in 24 cases, 11 years more than 5 cases. The group of 24 cases of genetic history, including paternal genetic 8 cases, maternal hereditary 11 cases, 2 cases of siblings and 1 case of aunt is the same