目的探讨心肌致密化不全的超声心动图及临床特点。方法选取20例心肌致密化不全患者,其中男性14例,女性6例;年龄3.5~81.0岁,平均年龄48.6岁。对其临床特点、心电图及超声心动图检查进行分析。结果临床症状以心慌、胸闷、气短等多见,占80%;1例出现偏瘫,2例合并先天性心脏病。90%伴有不同程度的心力衰竭。所有患者心电图出现异常,以心律失常多见(60%)。超声心动图检查所有患者均可探及纵横交错排列的肌小梁和大小不等深陷的小梁隐窝;非致密化心肌的厚度与致密化心肌的厚度比值(N/C)>2;彩色血流可见隐窝内血流与左心室相通。结论心肌致密化不全患者无特异临床表现及心电图改变,主要表现为反复发作的、进行性加重的心力衰竭和心律失常,栓塞事件少见。超声心动图可以显示该病的心肌结构,是该病的首选检查。 Objective To investigate the echocardiography and clinical features of myocardial densification. Methods Twenty cases of patients with myocardial densification were selected, including 14 males and 6 females, aged from 3.5 to 81.0 years with a mean age of 48.6 years. The clinical features, ECG and echocardiography were analyzed. Results Clinical symptoms were palpitation, chest tightness, shortness of breath and other more common, accounting for 80%; 1 case of hemiplegia, 2 cases of congenital heart disease. 90% with varying degrees of heart failure. All patients with abnormal ECG, arrhythmia more common (60%). In echocardiography, all patients were able to detect and traverse trabecular and trabecular crypts with varying depths; the ratio of non-densified to densified myocardium (N / C)> 2; Visible color blood flow in the crypt and left ventricular communication. Conclusions There is no specific clinical manifestations and ECG changes in patients with myocardial densification, mainly manifested as recurrent and progressive heart failure and arrhythmia, embolic events rare. Echocardiography can show the structure of the heart muscle, the disease is the preferred examination.