患者,女,34岁,因反复活动后喘憋伴发绀30余年入院。患者出生后1个月余父母即发现其喘憋,无发绀。至学龄期运动后出现口唇发绀、气急乏力。至医院就诊,反复检查心超示肺动脉高压,房水平少量分流,房间隔未见回声缺损,诊断“原发性肺动脉高压”,曾服用硝苯地平片治疗,因症状无明显 The patient, female, 34 years old, was admitted to hospital after more than 30 years of asthenia due to repeated activities. More than one month after the birth of the patient, the parents found wheezing and no cyanosis. To school age appear lips cyanosis, shortness of breath fatigue. To the hospital, repeated examination of the heart showed pulmonary hypertension, a small amount of shunt room level, no echo of atrial septal defect, diagnosis of “primary pulmonary hypertension”, had taken nifedipine tablets treatment, due to no significant symptoms