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作者研究了18例经组织学证实的脊髓血管母细胞瘤,男11例,女7例,起病年龄17~66岁,平均31岁。起始症状:感觉变化7例(38.9%),疼痛6例(33.3%),肢体无力5例(27.8%)。18例中硬脊膜内肿瘤19个,硬脊膜外肿瘤2个(来自椎体)。多发肿瘤3例。颈段和颈胸段肿瘤9例(50%),胸段8例(44.4%),腰段1例(5.6%)。9例(50%)并发囊肿。硬脊膜内肿瘤均发生于脊髓。硬脊膜内肿瘤中15个被全切,4个部分切除,其中2例经再次手术全切除。2例硬脊膜外肿瘤发源于椎体未能全切。术后13例(72.2%)病情改善,2例(11.1%)无变化,8例(16.7%)病情恶化。本组6例(33.3%)后颅凹亦发生了血管母细
The authors studied 18 cases of hemangioblastoma confirmed by histology, including 11 males and 7 females. The onset age was 17 to 66 years, with an average of 31 years. The initial symptoms: sensory changes in 7 cases (38.9%), pain in 6 cases (33.3%), limb weakness in 5 cases (27.8%). In 18 cases, there were 19 intradural tumors and 2 epidural tumors (from the vertebral body). There were 3 cases of multiple tumors. There were 9 cases (50%) of cervical and cervical thoracic tumors, 8 cases (44.4%) of thoracic segments, and 1 case (5.6%) of lumbar segments. Nine cases (50%) had cysts. Intradural tumors occur in the spinal cord. Of the 15 intradural tumors, 15 were completely resected and 4 were partially resected, of which 2 were completely resected. Two cases of epidural tumor originated from the vertebral body could not be completely cut. Thirteen patients (72.2%) had improvement in their condition, 2 (11.1%) had no change, and 8 (16.7%) had worsening disease. 6 cases (33.3%) of this group also had vascular capillaries in the posterior fossa