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本综合征自1825年Itard、1885年Tourette报道以来,发病机理至今尚无定论。其临床表现以爆破性不自主的发声和多发抽动并口出秽语为特征。多动症状常起始于头、面部,而后波及肢体近端和远端,可发生在讲话或工作之中,难受意志控制,但睡眠时消失,分散注意力时可稍减轻。均自童年起病,呈慢性病程,时轻时重,时发时停,很难完全治愈。本症临床较罕见,现特报道1例如下,并就有关问题略加讨论。患者,男,18岁,农民,住院号2166。右利。因面部与肢体反复抽动,伴不自主喉部发声约8年,加重4月,于1979年9月4日入院。患者自10岁起即有眨眼、歪嘴、伸舌、
The syndrome has been inconclusive since its publication by Itard in 1825 and reported by Tourette in 1885. Its clinical manifestations are characterized by explosive involuntary vocalizations and multiple twitching and verbal abuse. Hyperactivity symptoms often start in the head and face, and then spread to the proximal and distal limbs, can occur in the speech or work, uncomfortable will control, but disappear when sleep, distraction can be slightly reduced. Since childhood onset, a chronic disease course, when light weight, when the hair stopped, it is difficult to completely cure. The disease is more rare in clinical practice, is now reported 1 case below, and a little discussion on the issue. Patient, male, 18 years old, farmer, hospital number 2166. Right interest. Due to repeated facial and limb twitching, accompanied by involuntary laryngeal vocalizations for about 8 years, increased in April, on September 4, 1979 admission. Patients since the age of 10 have blinked, Wry mouth, tongue extension,