报道1例29岁女病人,儿时因患发作性黑蒙(blackouts)被错诊为癫痫,因发生致命性心律失常住院。患者在9岁时出现黑蒙发作,按癫痫予苯妥英治疗,其发作频率逐渐减少。29岁时继长时间腹泻后出现严重黑蒙住入急诊科。首次检查示室性心动过速,以后自发恢服了窦性心律。再次严重发作时经直流电击复律。2天后,连续发作4次尖端扭转性室性心动过速,每次持续5分钟,均自发缓解。其静息状态下心电图示QT期间延长至0.57S,无神经性耳 A 29-year-old female patient was reported. She was misdiagnosed as epilepsy with childhood blackouts due to fatal arrhythmia. Patients at 9 years of age appeared mammia attack, according to epilepsy to phenytoin treatment, the frequency of seizures gradually reduced. 29 years old after a long period of serious diarrhea after entering emergency department. The first examination showed ventricular tachycardia, after spontaneous recovery of sinus rhythm. Severe seizures by direct current shock law. Two days later, four consecutive episodes of torsades de pointes were performed spontaneously for 5 minutes each. The resting state ECG QT extended to 0.57S, no neurogenic ears