嗜铬细胞瘤是分泌儿茶酚胺的功能性肿瘤,多发生在一侧的肾上腺髓质。由于它的发生具有广泛的解剖基础,因此,随着肿瘤发生部位的不同,临床表现则有各种不同的特殊类型,常会造成诊断和治疗上的困难。Huener曾将它称为“10%的肿瘤”,即10%为恶性,10%多发,10%发生在肾上腺之外。国内许多报告对“10%的肿瘤”的说法提出了异议,并指出这些特殊类型的嗜铬细胞瘤,不但具有定位诊断和手术治疗上的困难,并有复发、恶变率高 Pheochromocytoma is a functional tumor that secretes catecholamines and occurs on one side of the adrenal medulla. Since its occurrence has a wide anatomical basis, there are various special types of clinical manifestations depending on the site of tumor, which often causes difficulties in diagnosis and treatment. Huener referred to it as “10% of tumors”, which means that 10% is malignant, more than 10% occurs, and 10% occurs outside the adrenal gland. Many domestic reports have disputed the claim of “10% of tumors” and pointed out that these special types of pheochromocytoma not only have difficulty in localization diagnosis and surgical treatment, but also have a high rate of recurrence and malignant transformation.