目前约一半胰腺内分泌肿瘤为“非功能性”,其余的则具有特异性生物学机能。全胰岛细胞肿瘤综合征罕见。最常见为胰岛素瘤,发病率约为年百万分之一;次为胃泌素瘤(Z-ES),发病率约为年百万分之0.5。其它肿瘤及综合征非常少见。基于用激素组化法测得肿瘤细胞特性,可将胰腺内分泌肿瘤分类。但大部分肿瘤由一种以上细胞组成,除非与临床症状和血浆激 At present, about half of the pancreatic endocrine tumors are “non-functional” and the rest have specific biological functions. Whole islet cell tumor syndrome is rare. The most common is insulinoma, with an incidence of about one millionth of an annual; followed by gastrinoma (Z-ES), with an incidence of about 0.5 parts per million. Other tumors and syndromes are very rare. Pancreatic endocrine tumors can be classified based on the characteristics of tumor cells measured by hormone histochemistry. But most tumors consist of more than one cell, except with clinical symptoms and plasma shock