发育不良的多囊肾(MDK)是新生儿腹部肿块中最常见的先天畸形之一。作者报告14例产前诊断的经验,以进一步在发病机理和疾病自然发展上提供资料,这些发现可以对病儿的预后及以后的处理提供更正确的意见。1985年9月～1988年8月在University ofVirginia Hospital14例胎儿被诊断MDK,所有诊断通过产前超声检查,均由产前诊断中心成员 Dysplastic polycystic kidney disease (MDK) is one of the most common congenital malformations in neonatal abdominal masses. The authors report on the experience of 14 cases of prenatal diagnosis to further provide information on the pathogenesis and natural development of the disease. These findings can provide a more accurate view of the prognosis and subsequent treatment of sick children. From September 1985 to August 1988, 14 fetuses were diagnosed with MDK at the University of Virginia Hospital. All diagnoses were confirmed by prenatal ultrasound and were performed by prenatal diagnostic centers