显微镜下型多血管炎(MPA)是抗中性粒细胞胞浆抗体(ANCA)相关性小血管炎(AASV)的一种,临床以肾、肺受累为其突出表现。我科曾收治1例以肺、肾、皮肤、关节损害为主要表现的儿童MPA,现报道如下。患儿女,13岁,因“咯痰带血3月余,镜下血尿、双下肢出血性皮疹1月余”于2005年3月入院 Microscopic polyangiitis (MPA) is a type of anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AASV) that is clinically characterized by kidney and lung involvement. My department had admitted to a case of lung, kidney, skin, joint damage as the main manifestation of children MPA, are reported below. Children, aged 13, were admitted to hospital in March 2005 for “more than 3 months of expectoration with blood, microscopic hematuria and bleeding of lower extremity in more than one month”