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目的 :阐明 Swyer- James综合征 (SJS)的病因 ,临床诊治等要点。方法 :报告 1例 SJS,并结合文献对该病病因 ,临床诊治及鉴别诊断等进行探讨。结果 :1例 12岁男孩 ,咳嗽咳痰 ,右肺纹理稀少 ,透亮度增高 ,容积缩小 ,吸气时心脏大部分位于右胸腔 ,呼气时回复 ,右肺门、动脉及分支变小。结论 :SJS是一罕见病 ,本质上是一种感染所致的闭塞性细支气管炎。主要临床表现有反复咳嗽、咳痰、咯血、喘息、呼吸困难。大部分症状与有否合并支扩有关。确诊主要依靠放射影像学检查 ,主要特点有肺透亮度增高、呼气相气体潴留、肺动脉变小等 ,可借此做鉴别诊断。SJS的治疗和预后与是否合并支扩有关 ,可内科或手术治疗。
Objective: To clarify the etiology, clinical diagnosis and treatment of Swyer-James syndrome (SJS). Methods: One case of SJS was reported, and the etiology, clinical diagnosis and differential diagnosis of the disease were discussed in combination with the literature. Results: A 12-year-old boy with cough and expectoration had scarce right lung texture, increased translucency, and reduced volume. Most of the heart was located in the right chest during inspiration and recovered on expiration. The right hilar, artery and branches became smaller. CONCLUSIONS: SJS is a rare disease that is essentially an episode of obliterative bronchiolitis. The main clinical manifestations are repeated cough, sputum, hemoptysis, wheezing, breathing difficulties. Most of the symptoms associated with whether or not merger expansion. The diagnosis depends mainly on radiographic examination, the main features of increased lung transparency, gas expiratory phase retention, pulmonary artery smaller, so as to make differential diagnosis. The treatment and prognosis of SJS is related to whether it is associated with branch expansion or can be treated by internal medicine or surgery.