听神经病谱系障碍(auditory neuropathy spectrum disorder,ANSD),也称为听神经病(auditory neuropathy,AN),是一种外毛细胞功能正常,而内毛细胞和听神经突触和/或听神经本身功能不良导致的听功能障碍[1,2]。ANSD典型的临床表现[3-7]是言语理解力受损,而言语觉察阈和纯音听阈可以正常,也可以严重受损。ANSD主要影响对快速变化声信号的处理,即听觉时间处理的能力[3]。 The auditory neuropathy spectrum disorder (ANSD), also known as auditory neuropathy (AN), is a disorder in which the outer hair cells function normally and the dysfunction of the inner hair cells and auditory synapses and / or the auditory nerve itself Listening dysfunction [1,2]. Typical clinical manifestations of ANSD [3-7] impaired verbal comprehension, and verbal and pure tone thresholds can be normal or severely impaired. ANSD mainly affects the handling of rapidly changing acoustic signals, the ability to process auditory time [3].