赘生性血管内皮增生病是一种罕见的血管疾患;具有伴发痴呆,卒中样发作及皮肤损害等一系列奇异神经系统症状的特征。全身血管内有广泛性血管内皮细胞增殖。文献上又称为“全身性增殖性血管内皮肥大病”和“弥散性恶性血管内皮增生”。本文报导1例对类固醇治疗神经系统症状有明显反应的此类病例。病例报告59岁妇女,右利手,因进行性痴呆及左侧轻偏瘫入院。两月前曾突然发作失语及右半身无力。一周后因多次发作语言不连贯曾在当地医院行脑扫描 Neoplastic angioendothelial hyperplasia is a rare vascular disorder characterized by a series of neuropathic symptoms associated with dementia, stroke-like episodes, and skin lesions. Extensive vascular endothelial cell proliferation in systemic blood vessels. The literature is also known as “systemic proliferative endothelium hypertrophy” and “disseminated malignant endothelium hyperplasia.” This article reports 1 case of steroid treatment of nervous system symptoms have obvious response to such cases. Case report 59-year-old woman, right hand, due to progressive dementia and left hemiparesis admission. Two months ago, a sudden onset of aphasia and weakness in the right half. A week later due to multiple episodes of language incoherent brain scan at a local hospital