Alport 综合征是累及肾脏和眼的一种综合病症。当晶体发生前锥形改变以后,可自行破裂,使视力急剧下降。笔者观察到1例,报告如下。患者张×男15岁半年前,视物不清,以右眼为重。双眼无外伤史。6岁时曾急性肾炎,10岁时耳聋。其兄1年前死于尿毒症。舅父25岁时死于尿毒症,否认眼病史。尿淡黄色,尿蛋白(++),白细胞(+),红细胞少数。两侧耳鼓膜正常。纯 Alport syndrome is a syndrome involving the kidney and eyes. When the crystal changes before the conical, can rupture themselves, so that sharp decline in visual acuity. I observed 1 case, the report is as follows. Zhang × male patients 15 years and a half years ago, depending on the material is not clear, with the right eye as the most important. No history of traumatic eyes. 6 years old had acute nephritis, 10 years old when deaf. His brother died of uremia 1 year ago. Uncle died of uremia 25 years old, denied the history of eye disease. Urine light yellow, urinary protein (++), white blood cells (+), a small number of red blood cells. Eardrum on both sides of normal. pure