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目的 提高对罕见病肺玻璃样变肉芽肿 (PHG)的认识。方法 对 1例经尸体解剖证实的PHG患者的临床资料进行分析 ,并结合文献复习。结果 PHG是一种罕见的肺疾病 ,临床表现为咳嗽、气短、胸痛、咯血、发热、疲劳 ,若病灶融合扩大可导致呼吸衰竭 ,胸部X线片特征是双肺多发肺结节 ,显微镜下结节的特点是由涡轮状或席纹状方式排列的胶原纤维组成 ,周围有炎性细胞浸润。病因及发病机制可能与免疫有关。结论 在双肺多发肺结节的鉴别诊断中应想到PHG的可能。PHG大多预后良好 ,目前尚无有效的治疗方法
Objective To improve the understanding of rare disease of pulmonary vitreous granuloma (PHG). Methods The clinical data of 1 PHG patient confirmed by autopsy were analyzed and reviewed. Results PHG is a rare pulmonary disease, clinical manifestations of cough, shortness of breath, chest pain, hemoptysis, fever, fatigue, if the fusion of the lesion can lead to respiratory failure, chest X-ray features are pulmonary pulmonary nodules, microscopic node The festival is characterized by collagen fibers arranged in a turbulent or zigzag pattern surrounded by inflammatory cell infiltration. Etiology and pathogenesis may be related to immunity. Conclusion The possibility of PHG should be considered in the differential diagnosis of pulmonary nodules. PHG most of the prognosis is good, there is no effective treatment