恶性蝾螈瘤(malignant triton tumor,MTT)是恶性神经鞘膜瘤的一种亚型,为含有横纹肌肉瘤成分的恶性神经鞘膜瘤。MTT的发生十分罕见,迄今为止,所报道病例只有200例左右,占全部恶性神经鞘膜瘤不到5%,而且国内外罕有颅内恶性蝾螈瘤的报道,我院近年收治1例,现结合文献复习如下。1病历摘要女,31岁。因头痛晕厥2d于2005-07在宜兴市人民医院行头颅CT检查提示为右顶叶脑肿瘤, Malignant triton tumor (MTT) is a subtype of malignant nerve sheath tumor, which is a malignant tumor of the sheath containing rhabdomyosarcoma. The occurrence of MTT is very rare, so far, reported only 200 cases, accounting for less than 5% of all malignant nerve sheath tumor, and rare intracranial malignant salamander tumor at home and abroad, our hospital admitted in recent years, 1 case, Combined with the literature review below. 1 medical record summary female, 31 years old. Due to headache syncope 2d in 2005-07 in Yixing City People’s Hospital head CT examination prompted the right parietal brain tumors,