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听神经瘤作为一种耳科疾患,既可以听神经本身的一种特发性病变出现,亦可以某种遗传性疾病的一个局部特殊表现而被察觉。近年来的研究发现,多发性神经纤维瘤(Neurofibromatosis,NF)患者常并发听神经病变,引起类似一般听神经瘤的临床表现。本文报告2例,并结合文献复习对该病的特点进行阐述,以供同道们参考。 1 病例报告 例1 女,24岁。因全身散在皮下结节14年,双耳持续性耳鸣、进行性听力下降、伴走路不稳5年入院。14年前无明显原因出现全身多处散在皮下结节,
Acoustic neuroma, as a otological disorder, not only appears as an idiopathic lesion of the nerve itself, but also as a local, specific manifestation of a hereditary disease. In recent years, the study found that patients with multiple neurofibromatosis (Neurofibromatosis, NF) often complicated by auditory neuropathy, causing similar general acoustic neuroma clinical manifestations. This article reports 2 cases, combined with the literature review of the characteristics of the disease described for the fellow reference. 1 case report 1 female, 24 years old. Due to systemic scattered subcutaneous nodules 14 years, binaural tinnitus, progressive hearing loss, with walking instability for 5 years admitted to hospital. 14 years ago, there was no obvious reason for multiple systemic scattered subcutaneous nodules,
