原发性肺动脉高压症属原因不明的血管性肺血管疾病。其20％～30％的患者可见自身免疫性疾病或伴有自身免疫性疾病症状,现将典型病例1例报道如下。 患者,女,31岁。因势力性心悸、气短1个月伴双手指遇冷时疼痛,于1990年3月15日收入院。既往无晕厥,无关节痛,无咳嗽、胸痛及咯血,无夜间阵发性呼吸困难。否认风心病、高血压病及慢性咳 Primary pulmonary hypertension is an unknown cause of vascular pulmonary vascular disease. Its 20% to 30% of patients with autoimmune or autoimmune disease can be seen in the symptoms, now a typical case reported as follows. Patient, female, 31 years old. Due to palpitations, shortness of breath 1 month with both hands when the cold pain, March 15, 1990 income hospital. No previous syncope, no joint pain, no cough, chest pain and hemoptysis, no paroxysmal nocturnal dyspnea. Denied rheumatic heart disease, hypertension and chronic cough