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目的提高对腹型系统性红斑狼疮(SLE)的认识,减少临床误诊误治。方法回顾性分析12例腹型SLE的临床资料分析临床特点。结果其中3例以腹部并发症为首发主要表现,开腹手术提示腹部血管炎,9例腹部并发症时间在SLE发病1个月~7年,1例因消化道穿孔手术治愈,1例因急性化脓性阑尾炎手术治疗,1例化脓性胆管炎术后死亡,其余保守治疗,共死亡4例。结论腹型SLE病情复杂,误诊误治发生率高,预后较差,提高对SLE的认识,选择合理的治疗措施是提高生存率的关键。
Objective To improve the understanding of abdominal type systemic lupus erythematosus (SLE) and reduce the misdiagnosis and misdiagnosis. Methods The clinical features of 12 cases of abdominal SLE were analyzed retrospectively. Results Among them, 3 cases had abdominal complications as the first major manifestation. Laparotomy indicated abdominal vasculitis. Nine cases of abdominal complications occurred within 1 month to 7 years after SLE. One case was cured by perforation of the digestive tract and one case suffered from acute Suppurative appendicitis surgery, 1 case of purulent cholangitis died, the remaining conservative treatment, a total of 4 patients died. Conclusions Abdominal SLE is complicated and the incidence of misdiagnosis and misdiagnosis is high and the prognosis is poor. To improve the understanding of SLE and choose the appropriate treatment measures are the keys to improve the survival rate.