论文部分内容阅读
我科近年来观察了两个家庭共14例家族性肥厚梗阻型心肌病(其中7例长期在本科就诊),猝死竟达9例,存活者临床上有一定特点。现将在本科就诊资料较完整的7例临床所见及家庭调查的7例结合文献复习报告如下。临床资料一、性别:男女各7例。二、年龄:最大46岁,最小11岁,20岁以下6例。三、临床症状及体征:见表1。四、X线检查:共7例,1例因脊椎严重畸形,房室大小难以判断未列入统计外,其余6例心脏增大者5例(83.3％),心胸比例均大于0.5:1,实测心脏表面积较预
In recent years, our family observed a total of 14 cases of familial hypertrophic obstructive cardiomyopathy (including 7 cases of long-term undergraduate treatment) in two families. There were 9 cases of sudden death, and the survivors had some clinical features. Now in the undergraduate medical information more complete in 7 cases of clinical findings and family survey of 7 cases combined with literature review report is as follows. A clinical data, gender: male and female in 7 cases. Second, the age: the largest 46 years old, the youngest 11 years old, 6 cases under the age of 20. Third, clinical symptoms and signs: See Table 1. Fourth, X-ray examination: a total of 7 cases, 1 case due to severe spinal deformity, atrioventricular dimension is difficult to judge not included in the statistics, the remaining 6 cases of cardiac enlargement in 5 cases (83.3%), cardiothoracic ratio were greater than 0.5: The measured heart surface area than the pre-