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虽然白塞氏病的神经系统并发症是该病死亡和病残的原因,但神经系统受累常数月至数年不能确诊。神经白塞氏病难以确诊的原因是因为神经系统检查和影像学的改变与许多其它疾病很相似,缺乏特异性诊断试验。而早期确诊神经白塞氏病,早期给予适当治疗,可以减少死亡率。 作者回顾性复习1985至1993年白塞氏病30例的医疗记录,其中神经白塞氏病9例(30%)。神经白塞氏病诊断依据:1.符合国际研究组关于白塞氏病的诊断标准(有口腔、生殖器溃疡、眼受累、反复皮损4主征中的3项)。2.腰穿证实有无菌性脑膜炎或神经影像异常。
Although the neurological complications of Behcet’s disease are the cause of death and disability of the disease, the nervous system can not be diagnosed for months to years of age. The reason that Nerve Behcet’s disease is difficult to diagnose is because neurological examination and imaging changes are similar to many other diseases and lack specific diagnostic tests. The early diagnosis of Neurocysticercosis, given appropriate early treatment, can reduce mortality. The authors retrospectively reviewed the medical records of Behcet’s disease from 1985 to 1993, of which 9 (30%) had Neurobechiasis. Nerve Behcet’s disease diagnosis is based on: 1. In line with international research group on Behcet’s disease diagnostic criteria (with oral and genital ulcers, ocular involvement, recurrent skin lesions 4 main symptoms in 3). 2. Waist wear confirmed aseptic meningitis or neurological abnormalities.