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病例资料患儿,女,11岁5个月,因“腹部膨隆9年,B超检查发现脾脏增大5年”入院。入院查体:一般情况可,生长发育差;腹部明显膨隆、张力稍高,腹壁可见静脉曲张;肝脏于肋下约3 cm处;脾脏呈Ⅲ度肿大,于肋下约20 cm处,质硬,活动度差,无压痛。腹部彩超检查示:肝脏最大斜径约14.5 cm长;脾脏肋间厚约7.6 cm,肋下达盆腔,向右达右侧腹,边界较清楚。腹部CT检查示:肝脏肿大;脾脏巨大,向下达盆腔,向右超过腹中线,边界清楚。胸部CT检查
Case data Children, 11 years and 5 months, due to “abdominal bulging 9 years, B-scan found spleen increased 5 years ” admission. Admission examination: the general situation may be, poor growth and development; significant bulging abdomen, tension slightly higher, abdominal varicose veins visible; liver in the ribs about 3 cm Department; spleen was Ⅲ degree enlargement in the ribs about 20 cm at the quality of Hard, poor activity, no tenderness. Abdominal ultrasonography showed: the largest oblique diameter of the liver is about 14.5 cm long; spleen intercostal thickness of about 7.6 cm, ribs under the pelvis, right to the right flank, the border more clearly. Abdominal CT examination showed: liver enlargement; huge spleen, down to the pelvic cavity, right over the midline abdomen, the border clear. Chest CT examination