原发肾脏横纹肌肉瘤国内外文献报告较少。现将2例报道如下。 例1,男,58岁。右腰胀痛伴低热20天。右肾区叩击痛。IVP及CT提示右肾占位病变,诊断肾癌;行右肾切除。肉眼观察,肿块位于肾上极呈结节状,切面灰白色、质嫩、中心出血坏死,直径5cm。镜下见瘤细胞呈蝌蚪样、梭形、未分化小圆形、椭圆形,核异型见病理性核分裂。 Primary renal rhabdomyosarcoma literature less reported at home and abroad. 2 cases are reported below. Example 1, male, 58 years old. Right lower back pain with fever for 20 days. Right kidney area percussion pain. IVP and CT tips right kidney lesions, diagnosis of renal cell carcinoma; right nephrectomy. Macroscopic observation, the tumor is located in the renal pole was nodular, cut gray, tender, bleeding hemorrhagic center, diameter 5cm. Microscopically see the tumor cells were tadpole-like, fusiform, undifferentiated small round, oval, nuclear abnormal see pathological mitosis.