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目的探讨12例木村病(Kimum’s disease,KD)患者的临床及病理特点,以提高对本病的认识。方法回顾性分析12例已确诊的KD患者的临床表现、实验室检查和病理检查资料。结果12例患者一般状态均较好,均有皮下肿块或淋巴结肿大,其中7例周围血嗜酸性粒细胞增高,6例行血清IgE测定,其中4例增高。全部病例均行活组织检查,结果均呈KD典型病理改变。12例中有1例患者合并有肺部和心脏病变。结论KD确诊有赖于活组织检查。本病可合并肺部和心脏病变,其中关系有待进一步探讨。
Objective To investigate the clinical and pathological features of 12 patients with Kumu disease (KD) to improve the understanding of this disease. Methods Retrospective analysis of 12 cases of KD patients have been diagnosed with clinical manifestations, laboratory tests and pathological examination data. Results All the 12 patients were in good condition with subcutaneous tumors or lymph nodes. Serum eosinophils were increased in 7 cases and serum IgE was detected in 6 cases, of which 4 cases were elevated. All cases were biopsy, the results were KD typical pathological changes. One of the 12 patients had lung and heart disease. Conclusion The diagnosis of KD depends on biopsy. The disease can be combined with lung and heart disease, the relationship to be further explored.