目的分析肾血管平滑肌脂肪瘤(错构瘤,AML)的CT表现,提高对常见及少见类型AML的诊断水平。方法回顾性分析11例AML患者的临床及影像资料。结果双侧AML2例,单侧9例,合并肾周及瘤内出血2例。典型者CT表现为肾内密度不均匀肿物,其内可见脂肪密度,1例不典型者可见病灶内少量脂肪。结论CT平扫必要时薄扫加增强扫描可对AML作出可靠的诊断。 Objective To analyze the CT manifestations of renal angiomyolipoma (AML) and to improve the diagnostic value of common and rare type AML. Methods Retrospective analysis of 11 cases of AML patients with clinical and imaging data. Results Two cases of bilateral AML, unilateral in 9 cases, combined with perirenal and intratumoral hemorrhage in 2 cases. Typical CT showed heterogeneous renal density within the tumor, the fat density can be seen inside, one case of atypical cases showed a small amount of fat lesions. Conclusions Thin-scan plus contrast-enhanced CT scan can make a reliable diagnosis of AML when necessary.