背景 只与在37℃最宜反应的IgA型自身抗体相关的自体免疫溶血型贫血(WAIHA)极为罕见。确诊时,IgA型自身抗体的特征是通常直接作用于Rh系统的抗原。然而,诸如IgG型自身抗体这一类自身抗体的主要特性无法鉴定。病例报告 本文报告一例3岁患儿,突发危及生命的WAIHA,最初予以红细胞输血和3mg/Kg剂量的类固醇激素治疗,慢慢地减少治疗剂量使 Background Autoimmune hemolytic anemia (WAIHA), which is associated only with IgA autoantibodies that respond optimally at 37 ° C, is extremely rare. At diagnosis, IgA-type autoantibodies are characterized by the antigens commonly acting directly on the Rh system. However, the major features of autoantibodies such as IgG autoantibodies can not be identified. Case Report This article reports a 3-year-old child with life-threatening WAIHA, initially treated with erythrocyte transfusions and 3 mg / kg of steroid hormone, and slowly reduced the dose