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目的:评价正颌正畸联合治疗Moebius综合征患者的牙颌畸形的远期疗效。方法:Moebius综合征患者3例,经正颌正畸联合会诊制订治疗计划,按照术前正畸、正颌手术、术后正畸的联合治疗模式进行系统治疗,随访1~6a。结果:Moebius综合征患者的牙颌特征主要表现为严重的骨性开畸形。对于牙颌畸形的治疗,主要是通过正颌正畸联合治疗进行矫正,但由于升颌肌群功能障碍,开矫正的复发倾向比较明显,需要术后密切随访治疗。结论:正颌正畸联合治疗能够矫正Moebius综合征患者严重的骨性开畸形,正颌手术后的长期随访对防止开的复发具有重要意义。
OBJECTIVE: To evaluate the long-term effect of orthognathic orthodontics in the treatment of dento-maxillofacial deformities in patients with Moebius’s syndrome. Methods: Three patients with Moebius syndrome were enrolled in the orthodontic treatment program. The patients were treated systematically according to the preoperative orthodontic, orthognathic surgery and postoperative orthodontic treatment. The patients were followed up for 1 ~ 6 years. Results: The dento-jaw features of patients with Moebius syndrome mainly manifested as severe bony open deformity. For the treatment of dento-maxillofacial deformity, orthognathic orthodontics is the most common method for orthodontic treatment. However, due to dysfunction of maxillary impacted jaw muscles, the recurrent tendency of recurrent orthodontic treatment is obvious, which requires close follow-up treatment. Conclusion: Orthodontics combined with orthodontic treatment can correct the severe osteomalacia in patients with Moebius syndrome. Long-term follow-up after orthognathic surgery is of great importance in preventing the recurrence of claudication.