特发性间质性肺炎(idiopathic interstitial pneumonias,IIP)指的是一组原因不明的间质性肺疾病,其发病机制复杂,诊治困难,并且发病率有逐年增高趋势,因此近年来国内外学者对该病从基础到临床展开了广泛而深入的研究,本文就此方面的研究进展情况予以阐述。1IIP的分类和诊断进展 Idiopathic interstitial pneumonias (idiopathic interstitial pneumonias, IIP) refers to a group of unexplained interstitial lung disease, its pathogenesis is complicated, diagnosis and treatment is difficult, and the incidence has increased year by year, so in recent years, scholars at home and abroad The disease from the foundation to the clinical research carried out extensive and in-depth, this article describes the progress of this research. 1IIP classification and diagnosis progress