致心律失常性右心室心肌病(ARVC)是一种以频繁发作的室性心动过速(VT)、心力衰竭和猝死为特征的遗传性心肌病,大多数病例40岁前甚至在儿童期死亡。随着研究的不断深入,此病的诊断方法和治疗策略取得了较大的进展。以下对致心律失常性右心室心肌病的诊断与治疗现状作一综述。 Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a hereditary cardiomyopathy characterized by frequent episodes of ventricular tachycardia (VT), heart failure, and sudden death, most of which died before the age of 40 and even in childhood . With the deepening of research, the disease diagnosis methods and treatment strategies have made great progress. The following on the diagnosis and treatment of arrhythmogenic right ventricular cardiomyopathy are reviewed.