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纤维肉瘤是纤维组织少见的恶性肿瘤,可发生于成人和儿童。它主要累及四肢,特别是腿、踝和脚。组织病理学家对区分“侵润性”纤维瘤病(一种也发生于婴儿的良性纤维瘤)和纤维肉瘤尚有疑议。这可解释一些先天性和婴儿纤维肉瘤不可预料的低转移率和高局部复发率的临床表现。本文对一例先天性纤维肉瘤的肿瘤作短期培养,并进行详尽的细胞遗传学分析。患儿出生时就发现右膝至小腿中部有一
Fibrosarcomas are rare malignant tumors of fibrous tissue and can occur in adults and children. It mainly affects the limbs, especially the legs, shins, and feet. Histopathologists are still skeptical about the distinction between “invasive” fibromatosis (a benign fibroid that also occurs in infants) and fibrosarcoma. This may explain the clinical picture of some unpredictable low metastases and high local recurrence rates of congenital and infantile fibrosarcoma. In this article, a case of a congenital fibrosarcoma tumor was cultured for a short period of time and a detailed cytogenetic analysis was performed. When the child was born, he found a right knee to the middle of the calf.