患者,女,9岁。因乏力,消瘦1年余,腹胀8个月,加重9个月,以肝脾肿大原因待查收住我科。既往未用过维生素K_1,无药物及食物过敏史,体检一般状态尚可,无黄疸,心肺未见异常,腹部膨性,肝肋下8.0cm,脾左肋下10.0cm,质中等度硬,表面光滑,无压痛,无腹水,实验室查肝功ZnTT26.9u,TTT17.3u,GPT11u,黄疸指数4u,二对半正常,血浆蛋白电泳总蛋白68g/L,凝血酶原时间16.5秒,延长。He49.7％,γ36.1％。 Patient, female, 9 years old. Due to fatigue, weight loss more than 1 year, abdominal distension for 8 months, increased 9 months to hepatosplenomegaly due to be admitted to live in our department. Previously used vitamin K_1, no history of drug and food allergies, physical examination was acceptable, no jaundice, no abnormal heart and lungs, abdominal swelling, liver ribs 8.0cm, spleen left ribs 10.0cm, medium and medium hardness, Smooth surface, no tenderness, no ascites, laboratory liver function ZnTT26.9u, TTT17.3u, GPT11u, jaundice index 4u, two pairs of normal, plasma protein electrophoresis total protein 68g / L, prothrombin time 16.5 seconds, extended . He49.7%, γ36.1%.