恶性卵黄囊瘤(malignant yolk sac tumor)是近年来已获公认的一个肿瘤单元。本瘤由原始生殖细胞来源,具有拟似胚胎发育过程中卵黄囊结构的分化特征。可为纯粹性,或与其它生殖细胞性肿瘤并存。本瘤不太少见,既往常误认为胚胎性癌或恶性畸胎瘤。主要发生于性腺,亦可见于骶尾部等靠近中线的其它部位。发生于睾丸者,多见于婴幼儿,其中两岁以内手术者予后较好。发生于卵巢和性腺以外部位者,则多见于儿童和青少年,恶性度高,予后不良。 Malignant yolk sac tumor (malignant yolk sac tumor) is a tumor unit has been recognized in recent years. The tumor originated from the primordial germ cells, with similar to the embryonic development of yolk sac structure differentiation characteristics. Can be pure, or co-exist with other germ cell tumors. The tumor is not uncommon, always mistaken for embryonal carcinoma or malignant teratoma. Occurs mainly in the gonads, can also be found in the sacrococcygeal and other parts near the midline. Occurred in the testes, more common in infants and young children, of whom surgery within two years of age is better. Occurred in ovarian and gonadal other than those who are more common in children and adolescents, high-grade, poor prognosis.