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作者检查了38例血管原始免疫细胞性淋巴结病(Angioimmunoblastic Lymphadenopathy简称AILD)的血和骨髓,其中男22例,女16例。平均年龄65岁(35~78岁)。32例大于50岁。临床表现:有发烧,消瘦、盗汗、搔痒。32例全身淋巴结肿大,肝脾肿大者分别为21及24例。21例有皮疹,6例纵隔扩大。血象:血色素6例男性低于10克,4例女性低于8克,其中5例男性Coombs试验阳性,3例有幼稚红细胞(32~700/100白细胞),红细胞形态正常。4/25例的网织红细胞增多伴Coombs试验阳性。34
The authors examined the blood and bone marrow of 38 patients with angioimmunoblastic Lymphadenopathy (AILD), including 22 males and 16 females. The average age of 65 years (35 to 78 years old). 32 cases were more than 50 years old. Clinical manifestations: fever, weight loss, night sweats, itching. 32 cases of generalized lymph nodes, hepatosplenomegaly were 21 and 24 cases. Twenty-one had rashes and 6 had mediastinal enlargement. Blood: 6 cases of hemoglobin in less than 10 grams of men, 4 cases of women less than 8 grams, 5 cases of male Coombs test was positive, 3 cases of naive erythrocytes (32 ~ 700/100 white blood cells), normal red blood cells. 4/25 cases of reticulocytosis with Coombs test positive. 34