先天性多囊肾是一种常见的染色体显性遗传性疾病。临床上并不罕见。按常染色体显性遗传方式 ,其发病率约为 1/ 10 0 0 ,约占慢性肾功能衰竭的 5 %～ 10 % [1] 。占终末期肾病的第三位。现将我院近 3ａ收治的 36例先天性多囊肾的诊断及治疗分析如下。1　临床资料本组病例均根据 Congenital polycystic kidney disease is a common chromosomal dominant genetic disease. Clinically not uncommon. According to autosomal dominant inheritance, the incidence of about 1/100, accounting for about 5% to 10% of chronic renal failure [1]. Accounting for the third of end-stage renal disease. Now in our hospital nearly 3 cases of 36 cases of congenital polycystic kidney diagnosis and treatment are as follows. 1 clinical data in this group of patients are based