报告肝外胆管癌按Ｌｏｎｇｍｉｒｅ分型，上段肛管癌占４３．６４％，中段胆管癌２１．８２％，下段胆管癌３４．５５％；有４２例得到病理诊断，浸润型２４例，结节型６例，乳头型１１例，９７．６２％为腺癌。手术切除１１例，切除率２６．１９％，其中上段胆管癌手术切除率１１．７６％；平均生存期１０．７８±９．６７月（ｘ±ＳＤ），但手术切除组生存期为２１．３５±１６．７３月（Ｘ±ＳＤ），疗效最好，胆肠内引流次之。并对肝外肛管癌的早期诊断、治疗方法选择以及是否术前施行ＰＴＣＤ等问题进行了讨论。 According to the Longmire classification of extrahepatic bile duct carcinoma, the upper anal canal cancer accounted for 43.64%, the middle bile duct carcinoma was 21.82%, and the lower bile duct carcinoma was 34.55%. There were 42 pathological diagnoses, 24 infiltrating types, and nodules. Type 6 cases, 11 cases of papillary type, 97.62% of adenocarcinoma. Surgical resection was performed in 11 cases with a resection rate of 26.19%. The resection rate of the upper segment of the bile duct carcinoma was 11.76%. The mean survival time was 10.78±9.67 months (x±SD), but the survival time in the surgical resection group was 21. 35 ± 16.73 months (X ± SD), the best effect, followed by drainage of biliary intestine. The issues of early diagnosis of extrahepatic anal canal cancer, choice of treatment methods, and whether preoperative PTCD was performed were discussed.