目的总结女性中肾管残件肿瘤临床组织病理学特征。方法对2例中肾管残件肿瘤患者手术标本进行组织病理学及免疫表型分析。结果 2例患者均无特异临床症状;肿瘤位于输卵管系膜及阔韧带,瘤细胞呈紧密小管状排列,细胞形态较温和,核分裂像罕见;管周基底膜PAS染色阳性,肿瘤细胞vimentin、α-inhibin、肌酸激酶弥漫阳性。结论女性中肾管残件肿瘤诊断需依靠组织病理学、免疫表型及发生部位。 Objective To summarize the clinical histopathological features of residual renal and renal tumor in women. Methods Histopathological and immunophenotypic analysis of 2 surgical specimens of patients with residual nephrouretesis was performed. Results There were no specific clinical symptoms in the two cases. The tumor was located in the tubal and broad ligament of the ovary. The tumor cells were arranged in a tight tubular arrangement. The morphology of the tumor was mild and the mitotic figures were rare. The PAS staining of the perivascular basis was positive. The expression of vimentin, inhibin, creatin kinase diffuse positive. Conclusion The diagnosis of nephrouretes in women depends on histopathology, immunophenotype and site of occurrence.