神经纤维瘤病具有遗传特性,临床上病变多种多样.中枢神经、周围神经、内脏、骨骼和皮肤都可发生.巨大外周型神经纤维瘤的手术比较困难,国内文献报道甚少.本院从1962～1985年间共手术治疗了头颈、躯干和四肢巨大神经纤维瘤11例,10例获访,除1例恶变死亡外其他9例效果比较满意.现报告如下。 Neurofibromatosis is genetic in nature and has a variety of clinical lesions. The central nervous system, peripheral nerves, internal organs, bones, and skin can all occur. Surgery for giant peripheral neurofibromas is difficult, and domestic literature is rarely reported. From 1962 to 1985, 11 cases of giant neurofibromas of the head and neck, trunk, and extremities were treated surgically. 10 cases were visited. Except for 1 case of malignant death, 9 cases were satisfactory. The present report is as follows.