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肝豆状核变性是一种遗传性铜代谢障碍性疾病，在神经系统症状出现之前临床表现形式多样，易误诊为其它疾病。自１９９０～１９９７年以来我科共收治肝豆状核变性误诊病例１１例，现将其分析报道如下。１临床资料１．１一般资料患者１１例，男７例，女４例。年龄：１岁以上２例
Hepatolenticular degeneration is a hereditary disorder of copper metabolism that manifests itself in a variety of clinical manifestations prior to the appearance of neurological symptoms and misdiagnosis of other diseases. Since 1990 to 1997 our department received a total of 11 cases of Wilson’s disease misdiagnosed cases, now the analysis reported as follows. 1 Clinical data 1.1 General Information 11 patients, 7 males and 4 females. Age: 1 year old and 2 cases