大疱性表皮松解症是一种罕见的遗传性皮肤病。1983年3月我院遇到一例,现报导如下: 病史:患儿杜××,2（3/12）岁,甘肃榆中人。于出生后40天开始在足跟、手指背、腕部出现松软疱疹,无红肿发热现象,数天后又在面颊、四肢、肩背部相继出现蚕豆大至孩拳头大大疱,疱液清亮或含少许血液, Epidermolysis bullosa is a rare hereditary dermatosis. In 1983 March a case of our hospital, are reported as follows: History: children Du × ×, 2 (3/12) years old, Gansu Yuzhong. 40 days after birth in the heel, finger back, wrists appear soft herpes, no redness fever, a few days later in the cheeks, limbs, shoulder and back have big fist bullous big blisters, blister fluid clear or containing a little blood,