婴幼儿黑色素性神经外胚瘤甚为少见,此瘤典型地发生于一岁以内的婴儿的上颌骨前部。国内文献报告仅见4例。现将我科所见一例报告如下: 患者,女,5岁,其母诉该女自出生后一个月即发现,上门牙根部长一黄豆大肿物,数日后长至其拇指大小,一个月后长至鸭蛋大小,以后未见继续增大。当时曾到当地医院就诊,因不愿手术而放弃治疗。检查:上唇外翻,肿物占据上颌骨前的区牙槽齿龈间。表面光滑,周围界限清楚,极度前突,质硬、固定。腭侧肿胀,此区ⅡⅡ牙齿消 Infant and young children with melanotic neuroepithelial neoplasia are rare, and this tumor typically occurs in the anterior part of the maxilla in infants up to one year old. Only 4 cases were reported in domestic literature. A case report from our department is as follows: The patient, female, is 5 years old. The mother complained that the woman had found a large tumor of a soy bean in the mouth of the upper incisor one month after birth. It grew to the size of her thumb a few days later. As long as the size of the duck egg, no increase in the future has been observed. At that time, he went to a local hospital and abandoned treatment because he did not want surgery. Check: The upper lip is ectropion, and the tumor occupies between the alveolar gingiva in the area of ​​the maxilla. The surface is smooth, the boundary is clear, extreme protrusion, hard and fixed. Swelling of the temporal side, II II tooth elimination in this area