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病历摘要患者,男,58岁。主因反复皮肤粘膜出血,间断血便6年,加重伴双下肢浮肿2月余,于1988年10月27日入院。 83年5月皮肤出现0.5×0.5cm~2—4×4cm~2大小不等的散在紫斑,无痛痒,压之不褪色。间断暗红色便。偶有牙龈出血及痰中带血。在当地医院查Hb6~8克%,WBC 1900~2700/mm~3,红系明显增生,伴轻度类巨幼变,巨核系正常。用铁剂,Vit B_(12)叶酸及大力补等治疗无效,于1984年8月首次入我院血
Patient summary, male, 58 years old. Mainly due to repeated skin and mucous membrane bleeding, intermittent bloody stool 6 years, increased with lower extremity edema more than 2 months, on October 27, 1988 admission. May 83 skin appeared 0.5 × 0.5cm ~ 2-4 × 4cm ~ 2 scattered purple spots of varying sizes, itchy, the pressure of the fade. Dark red intermittent it. Occasional gingival bleeding and bloody sputum. Hb6 ~ 8% in the local hospital check, WBC 1900 ~ 2700 / mm ~ 3, erythroid hyperplasia, with mild megaloblastic degeneration, megakaryocyte normal. With iron, Vit B_ (12) folic acid and vigorously complement treatment ineffective, in August 1984 for the first time into our hospital blood