原发性腹膜后肿瘤(PRT)是指起源于腹膜后间隙的肿瘤,是较少见的疾病。可起源于腹膜后间隙的脂肪、平滑肌、结缔组织、血管、筋膜、神经组织、淋巴组织和胚胎残留组织等,不包括腹膜后间隙的各器官肿瘤和腹膜后转移肿瘤[1]。PRT发病率低,占全身肿瘤的0·07%～0·2%[2]。由于腹膜 Primary retroperitoneal tumor (PRT) refers to tumors that originate in the retroperitoneal space and is a less common disease. Peritoneal space can be derived from the fat, smooth muscle, connective tissue, blood vessels, fascia, nerve tissue, lymphoid tissue and embryonic residual tissue, etc., not including retroperitoneal space of organs and retroperitoneal tumor metastasis [1]. The incidence of PRT is low, accounting for 0. 07% -0.2% of the total body tumors [2]. Because of the peritoneum