目的分析烟雾病(MMD)的临床及数字减影血管造影(DSA)特征。方法分析18例烟雾病患者的资料,观察其临床及DSA特点。结果本组病例多为青壮年起病,女性居多,主要有脑梗死、脑出血和短暂脑缺血发作起病形式,临床表现为肢体麻木、无力、头痛、智力减退等症状;DSA在脑底动脉环发现血管闭塞、狭窄及烟雾状毛细血管网形成。结论对于青壮年发作的脑卒中患者要考虑MMD的可能。目前仍依靠数字减影血管造影确诊。 Objective To analyze the clinical and digital subtraction angiography (DSA) features of moyamoya disease (MMD). Methods The data of 18 patients with moyamoya disease were analyzed and their clinical features and DSA characteristics were observed. Results Most of the patients in this group were young and middle-aged, mostly female, with the main forms of onset of cerebral infarction, cerebral hemorrhage and transient ischemic attack. The clinical manifestations were limb numbness, weakness, headache, mental retardation and other symptoms. Artery ring found vascular occlusion, stenosis and smoke-like capillary network formation. Conclusion The possibility of MMD should be considered in stroke patients with young adults. Still rely on digital subtraction angiography confirmed.