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目的探讨超声心动图检查在胎儿完全性肺静脉异位引流(TAPVC)诊断中的临床价值。方法回顾性分析11例TAPVC胎儿的超声心动图特征以及产后超声心动图检查或引产后尸检的结果。结果 11例TAPVC胎儿(心上型7例,心内型3例,心下型1例),3例属于单发畸形,8例并发其他心内外畸形。超声心动图正确诊断9例,准确度约为81.82%(9/11),漏诊2例。典型的声像图特征:四腔心切面左心稍小于右心,左房顶壁光滑,无肺静脉开口,4条肺静脉在左房后方汇入共同肺静脉干,并经引流血管汇入右房,相应引流血管扩张。结论超声心动图检查是产前诊断TAPVC的可靠方法,有利于孕妇作出优生优育选择,具有较高的临床应用价值。
Objective To investigate the clinical value of echocardiography in the diagnosis of complete anomalous pulmonary venous drainage (TAPVC). Methods The echocardiographic features of 11 TAPVC fetuses and the results of postpartum echocardiography or post-induction autopsy were retrospectively analyzed. Results Eleven TAPVC fetuses (7 in cardiac type, 3 in cardiac type and 1 in cardiac type), 3 had single malformations and 8 had other intracardiac and cardiac deformities. Echocardiography correct diagnosis of 9 cases, the accuracy of about 81.82% (9/11), missed diagnosis in 2 cases. Typical features of the sonogram: left ventricular heart four chamber slightly less than the right heart, left atrial top wall smooth, no pulmonary vein openings, 4 pulmonary veins in the left atrial rear into the common pulmonary vein and the drainage of blood into the right atrium, Corresponding drainage of blood vessels to dilate. Conclusion Echocardiography is a reliable method for prenatal diagnosis of TAPVC, which is conducive to the selection of prenatal and postnatal care in pregnant women and has high clinical value.