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患者,女性,50岁。因劳累后心慌气短,口唇发绀35余年。缘于10岁时剧烈活动后心慌气短,口唇较常人紫绀,蹲居后症状缓解。19岁结婚,21~28岁顺产四胎,子女及爱人均健在。孕期心慌气短加重。口面及四肢均紫绀加重。本次因阵发性左侧胸痛5小时,持续性心慌气短而入院。体检:全身皮肤粘膜明显紫绀,唇甲尤著,有杵状指趾,心前区稍隆起,心率98,律整,胸骨左缘第2~4肋间可闻及Ⅲ级以上收缩期吹风样杂音,伴有震颤,两肺(-)腹软,肝于右肋缘下2cm,双下肢指凹性水肿。心电图示:(1)肺型P波,(2)电轴右偏,(3)右室肥厚;(4)心肌缺血。X线胸片:心影呈靴形,主动脉升弓部增宽,两肺门动脉纤细,肺血减少。在我院行心脏
Patient, female, 50 years old. Flustered because of fatigue after a short time, lips cyanosis more than 35 years. Due to 10-year-old after the violent activities of palpitation shortness of breath, lips more common cyanosis, symptoms after croupation ease. 19-year-old married, 21 to 28-year-old with four-births, children and lovers are alive. Flustered during pregnancy aggravate shortness of breath. Facial and limbs are cyanotic aggravate. The paroxysmal left chest pain for 5 hours, persistent flustered shortness of breath and admitted to hospital. Physical examination: systemic skin and mucous membrane was cyanotic, especially in the labia minora, a clubbed toe, slightly elevated precordial area, heart rate 98, law, sternal left margin 2 ~ 4 intercostal can smell and Ⅲ above the systolic hair style Noise, accompanied by tremor, both lungs (-) abdomen soft, liver 2cm under the right costal margin, both lower extremity means concave edema. ECG shows: (1) pulmonary P wave, (2) axis deviation, (3) right ventricular hypertrophy; (4) myocardial ischemia. X-ray: heart shadow was boot-shaped, aortic arch widening, two pulmonary artery slender, reduced lung blood. Heart in our hospital