Steiner 氏病,也称萎缩性肌强直、营养不良性肌强直,是一种比较少见的遗传性肌病,我国仅见1953年黄克维等报告一例,1980年罗成仁报告4例。我们曾迂一家系3人发病,且并发白内障,现报告如下:例1:王某某,女 35岁,农民。患者以左眼看不见5年,门诊以并发性白内障收入院。入院时视力 OD0.2 OS Lp(+)光定 Steiner’s disease, also known as atrophic myotonia, malnutrition myotonia, is a relatively rare genetic myopathy, only seen in China in 1953, Huang Kewei and other reports of a case in 1980, Luo Chengren reported 4 cases. We have a pedigree Department 3 Department of onset, and concurrent cataract, are as follows: Example 1: Wang Moumou, female 35 years old, farmer. Patients can not see the left eye for 5 years, outpatient hospital with complicated cataract. Vision at admission OD0.2 OS Lp (+) light set