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目的探讨乳腺炎性肌纤维母细胞瘤的临床病理特征和鉴别诊断。方法对1例乳腺炎性肌纤维母细胞瘤进行临床、组织学和免疫组化观察,并复习相关文献。结果患者女性,62岁。左乳腺扪及一肿块8个月,边界尚清。组织学显示,黏液背景下瘤细胞以梭形细胞为主,细胞无异型性,核分裂象少见。间质内见大量淋巴细胞,浆细胞浸润,血管丰富,局部有胶原化。免疫组化:梭形细胞vimentin中等(+),SMA、actin和ALK(+);CK、34βE12、S-100、myogenin、MBP和CD34(-)。结论炎性肌纤维母细胞瘤是一种特殊类型的间叶性肿瘤,罕见于乳腺,应与梭形细胞癌、纤维瘤病、瘢痕、结节性筋膜炎等相鉴别。
Objective To investigate the clinicopathological characteristics and differential diagnosis of mastitic myofibroblastic tumor. Methods One case of mastitic myofibroblastoma was observed by clinical, histological and immunohistochemical methods, and the related literatures were reviewed. Results Patient female, 62 years old. Left breast palpable mass a month, the boundary is clear. Histology showed that spindle cells dominated tumor cells in the mucus background, cells were nonspecific, and mitotic figures were rare. Interstitial see a large number of lymphocytes, plasma cell infiltration, vascular rich, local collagen. Immunohistochemistry: spindle cells vimentin medium (+), SMA, actin and ALK (+); CK, 34βE12, S-100, myogenin, MBP and CD34 (-). Conclusion Inflammatory myofibroblastoma is a special type of mesenchymal tumor, which is rare in breast and should be differentiated from spindle cell carcinoma, fibromatosis, scar and nodular fasciitis.