强直性肌萎缩(简称DM)是最常见的成年型肌肉萎缩。其发病率(2.4～5.5/10万),在所有类型肌肉萎缩中最高。由于肢体远端进行性肌张力减弱,本病常导致残废,因心脏传导障碍,故可出现猝死。本世纪初以来,白内障被认为是DM的一个必备特征。Vogh曾运用裂隙灯显微镜活组织检查,描述了彩虹色颗粒及玫瑰花形晶体囊膜下混浊,这些都是DM的显著特 Myotonic dystrophy (DM) is the most common form of adult muscle atrophy. The incidence (2.4 to 5.5 / 100,000) was the highest among all types of muscle atrophy. Due to the distal limb weakening of the muscle tone, the disease often lead to disability, due to cardiac conduction disorders, it can occur sudden death. Cataracts have been considered as an essential feature of DM since the beginning of this century. Vogh used slit-lamp microscopy to characterize sub-capsular opacities of rainbow-colored particles and rose-shaped crystals, all of which are notable for DM