血友病和第Ⅸ因子缺乏症血友病和第Ⅸ因子缺乏症是两种凝血障碍最普通的遗传性疾患。其发病率不高,但这些患者给护理、职业、教育和恢复工作带来重大问题。现在公认,血友病和第Ⅸ因子缺乏症的大量出血是由于特殊的蛋白质:抗血友病因子(AHF、抗血友病球蛋白或第Ⅷ因子)及第Ⅸ Hemophilia and Factor IX Deficiency Hemophilia and Factor IX deficiency are the most common hereditary disorders of both coagulopathy. Their morbidity is low, but these patients pose major problems in their care, occupation, education and rehabilitation. It is now recognized that the substantial hemorrhaging of hemophilia and factor IX deficiency is due to the specific proteins: antihemophilic factor (AHF, antihemophilic globulin or factor VIII) and IX