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女性,18个月,无特殊家族史和既往史。初诊于1988年6月10日。3个月前在左大阴唇处出现半颗米粒大小的皮疹,以后逐渐增大。查体时见左大阴唇处有一个4.5mm×4mm 大小,呈半球状隆起弹性软,皮软有淡黄红色丘疹。其它部位未见类似皮疹及色素斑。无自觉症状。病理组织学所见从表皮到真皮的下层,见无被膜组织的与周围界限清晰的细胞团。病变部位的表皮变薄。细胞团主要由细胞体发亮的泡沫细胞聚集而成,并有许多 Touton 型巨细胞混杂在这些细胞中,细胞质用希夫过碘酸染色呈弱阳性。用免疫组织化
Women, 18 months, no special family history and past history. Newly diagnosed on June 10, 1988. A half-size rice rash appeared in the left labia majora 3 months earlier and gradually increased. At the time of the examination, the left labia majora had a size of 4.5 mm x 4 mm. The hemispherical bulge was elastic and soft, and the soft skin had pale yellowish red papules. No similar rashes and pigment spots were found in other sites. No symptoms. Histopathology seen from the epidermis to the lower layers of the dermis, see a clear cell mass with no surrounding tissue. The epidermis of the lesion is thinned. Cell clusters are mainly composed of foam cells with bright cell bodies, and many Touton giant cells are intermingled in these cells. The cytoplasm is weakly positive with Schiff’s periodic acid staining. Immunohistochemistry